Mucopolysaccharidosis type VI

Lysosomal storage disorder linked to a deficiency of the arylsulfatase B enzyme

Symptoms
Dwarfism and facial dysmorphia, hindlimb paresis or paralysis due to spinal cord compression, bilateral pain at flection and extension of the joins, multifocal neurologic deficits, corneal clouding and retinal atrophy.

Gene involved
ARSB

Mutation tested
c.1427T>C

Transmission mode : Autosomal recessive
Age of onset : Between 6 and 8 weeks old

Publication : Yogalingam et al. (1996). Feline mucopolysaccharidosis type VI - characterization of recombinant n-acetylgalactosamine 4-sulfatase and identification of a mutation causing the disease.