GM2 Gangliosidosis

Gene involved
HEXB

Mutation tested
c.283delG

Transmission mode : Autosomal recessive

Publication : Rahman et al. (2012). A frameshift mutation in the canine HEXB gene in toy poodles with GM2 gangliosidosis variant 0 (Sandhoff disease).

Gene involved
HEXB

Mutation tested
c.618-620delCCT

Transmission mode : Autosomal recessive

Publication : Wang et al. (2018). Canine GM2-Gangliosidosis Sandhoff Disease Associated with a 3-Base Pair Deletion in the HEXB Gene.

Concerned breeds :

Gene involved
HEXA

Mutation tested
c.967G>A

Transmission mode : Autosomal recessive

Publication : Sanders et al. (2013). GM2 gangliosidosis associated with a HEXA missense mutation in Japanese Chin dogs: a potential model for Tay Sachs disease.

Concerned breeds :